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Diffuse lipofibromatosis of the lower extremity masquerading as a vascular anomaly.

Identifieur interne : 006324 ( Main/Exploration ); précédent : 006323; suivant : 006325

Diffuse lipofibromatosis of the lower extremity masquerading as a vascular anomaly.

Auteurs : Arin K. Greene [États-Unis] ; Julie Karnes ; Horacio M. Padua ; Birgitta A. Schmidt ; James R. Kasser ; Brian I. Labow

Source :

RBID : pubmed:19461290

Descripteurs français

English descriptors

Abstract

Lipofibromatosis is a slow-growing, childhood soft-tissue neoplasm that is often confused with other conditions. We report a patient with lipofibromatosis causing extremity enlargement at birth. The lesion initially was thought to be a vascular anomaly or lipedema on clinical and MRI examination. When involving the lower extremity, diffuse lipofibromatosis must be differentiated from more common causes of lower limb enlargement in children: lymphatic malformation, lymphedema, or lipedema. Compared with these more frequent conditions, lipofibromatosis usually causes less morbidity. Management of the tumor includes observation or excision. Because complete extirpation of the lesion is difficult, the recurrence rate is high.

DOI: 10.1097/SAP.0b013e3181a13df6
PubMed: 19461290


Affiliations:


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Le document en format XML

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